Surgery>>>>>Congenital Heart Disease
Question 6#

Which of the following is a true surgical emergency in a newborn? 

A. Tetralogy of Fallot
B. Truncus arteriosus
C. Total anomalous pulmonary venous connection (TAPVC)
D. COA

Correct Answer is C

Comment:

Total anomalous pulmonary venous connection (TAPVC) occurs in 1 to 2% of all cardiac malformations and is characterized by abnormal drainage of the pulmonary veins into the right heart, whether through connections into the right atrium or into its tributaries. Accordingly, the only mechanism by which oxygenated blood can return to the left heart is through an ASD, which is almost uniformly present with TAPVC. Unique to this lesion is the absence of a definitive form of palliation. Thus, TAPVC represents one of the only true surgical emergencies across the entire spectrum of congenital heart surgery.